Cite this article as: Aktaş B, Gümüş D, Tunalı A, Kunter Z, Adrovic A. Mevalonate kinase deficiency/hyperimmunoglobulin D syndrome in a differential diagnosis of periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome and familial mediterranean fever: A case report. Turk Arch Pediatr. 2022;57(3):365-367.