Turkish Archives of Pediatrics
Case Report

Anomalous left coronary artery from pulmonary artery (ALCAPA) in asymptomatic 11-year-old case

1.

İstanbul University, Cerrahpaşa Medical Faculty, Department of Pediatrics, Division of Pediatric Cardiology, İstanbul, Turkey

Turk Arch Pediatr 2012; 47: 298-301
DOI: 10.4274/tpa.619
Read: 775 Downloads: 729 Published: 11 December 2020

Origin of the left coronary artery from the pulmonary trunk [Anomalous origin of the Left Coronary Artery from the Pulmonary Artery (ALCAPA)] is a rare congenital heart defect. ALCAPA is one of the common causes of myocardial ischemia or infarction in infants and children. In this report, we present an eleven-years-old patient presenting with murmur and accompanied by echocardiographic findings of dilated cardiomyopathy and angiocardiographic investigation that revealed left coronary artery originating from the pulmonary artery. (Turk Arch Ped 2012; 47: 298-301)


Pulmoner arterden kaynaklanan sol koroner arter anomalisi (ALCAPA) olan 11 yaşında yakınmasız olgu 

Pulmoner arterden çıkan anormal sol koroner arter [“Anomalous origin of the Left Coronary Artery from the Pulmonary Artery” (ALCAPA)] nadir görülen bir doğuştan kalp anomalisidir. Süt çocukları ve çocuklarda ALCAPA miyokardiyal iskemi veya infarktüsün sık karşılaşılan sebeplerinden birisidir. Bu makalede hastanemize üfürüm duyulması nedeniyle başvuran ve ekokardiyografik olarak dilate kardiomyopati ve kateter-anjiyografisinde sol koroner arterin pulmoner arterden köken aldığı görülen 11 yaşındaki bir hastamız sunulmuştur. (Türk Ped Arş 2012; 47: 298-301)

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